Documentation & Coding Risks
Avoid these common issues when documenting Alport Syndrome.
Frequently Asked Questions
The ICD-10 code for Alport syndrome is Q87.81, used when the diagnosis is confirmed through genetic testing or clinical criteria.
Alport syndrome is diagnosed through genetic testing for COL4A3, COL4A4, or COL4A5 mutations, along with clinical criteria such as hematuria and hearing loss.
Related condition guides
Documentation requirements, coding pitfalls and FAQs for conditions coded with Q87.81.