What is the ICD-10 code for hemophilia?

The ICD-10 code for hereditary hemophilia A is D66, which requires documentation of hereditary factor VIII deficiency.

How to code acquired hemophilia?

Use ICD-10 code D68.311 for acquired hemophilia, confirmed by the presence of factor VIII inhibitors.

ICD-10 Coding for Bleeding Disorder(D66, D68.0, D50.0)

Save

Explore detailed ICD-10 coding guidelines for bleeding disorders, including hemophilia and von Willebrand disease. Learn about documentation requirements and coding pitfalls.

Also known as:

Coagulation DefectHemorrhagic Disorder

Related ICD-10 Code Ranges

Complete code families applicable to Bleeding Disorder

D50-D89Primary Range

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

→

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

Code	Description	When to Use	Key Documentation
D66	Hereditary factor VIII deficiency	Use when hereditary factor VIII deficiency is confirmed by lab tests.	Factor VIII activity <40% Normal vWF levels
D68.0	Von Willebrand's disease	Use when von Willebrand's disease is confirmed by specific antigen and cofactor levels.	vWF antigen <50 IU/dL Ristocetin cofactor <30 IU/dL

Primary ICD-10-CM Codes

Hereditary factor VIII deficiency

D66Billable

Von Willebrand disease

D68.0

Differential Codes

Alternative codes to consider when ruling out similar conditions

Acquired hemophiliaD68.311

Qualitative platelet defectsD69.1

Documentation & Coding Risks

Avoid these common issues when documenting Bleeding Disorder.

Using D69.1 without platelet studies

Impact

Clinical: Misdiagnosis of platelet disorders., Regulatory: Non-compliance with coding standards., Financial: Potential for denied claims.

Mitigation

Verify platelet function tests before coding.

Coding D68.2 for acquired hemophilia

Impact

Reimbursement: Incorrect DRG assignment may lead to underpayment., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate clinical data representation.

Mitigation

Use D68.311 + T45.515A for acquired cases.

Incorrect Hemophilia Coding

Impact

Risk of coding hereditary hemophilia as acquired.

Mitigation

Require genetic testing documentation.

Frequently Asked Questions

Documentation requirements, coding pitfalls and FAQs for conditions coded with D66.

Primary Code

D66

Hereditary factor VIII deficiency

Quick Navigation

ICD-10 codes8

Coding risks3

FAQs2

ICD-10 Coding for Bleeding Disorder(D66, D68.0, D50.0)

Documentation & Coding Risks

Frequently Asked Questions

What is the ICD-10 code for hemophilia?

How to code acquired hemophilia?

Related condition guides