What is the ICD-10 code for Ehlers-Danlos Syndrome?

The ICD-10 code for unspecified Ehlers-Danlos Syndrome is Q79.60. Specific types have their own codes: Q79.61 for Classical, Q79.62 for Hypermobile, and Q79.63 for Vascular EDS.

How do you code hypermobile Ehlers-Danlos Syndrome?

Hypermobile Ehlers-Danlos Syndrome is coded as Q79.62, requiring documentation of a Beighton score ≥5/9 and systemic manifestations.

ICD-10 Coding for Ehlers-Danlos Syndrome(Q79.60, M35.7, Q79.61)

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Comprehensive guide to ICD-10 coding for Ehlers-Danlos Syndrome, including specific codes for Classical, Hypermobile, and Vascular types.

Also known as:

EDSEhlers-Danlos

Related ICD-10 Code Ranges

Complete code families applicable to Ehlers-Danlos Syndrome

Q00-Q99Primary Range

Congenital malformations, deformations and chromosomal abnormalities

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Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

Code	Description	When to Use	Key Documentation
Q79.60	Ehlers-Danlos syndrome, unspecified	Use when the specific type of EDS is not documented or known.	Generalized joint hypermobility Skin hyperextensibility
Q79.61	Classical Ehlers-Danlos syndrome	Use when classical EDS is confirmed by genetic testing and clinical criteria.	COL5A1 or COL5A2 mutation Skin hyperextensibility Atrophic scarring
Q79.62	Hypermobile Ehlers-Danlos syndrome	Use when hypermobile EDS is confirmed by clinical criteria.	Beighton score ≥5/9 Systemic manifestations such as chronic pain or dysautonomia
Q79.63	Vascular Ehlers-Danlos syndrome	Use when vascular EDS is confirmed by genetic testing and clinical criteria.	COL3A1 mutation Family history of vascular rupture

Primary ICD-10-CM Codes

Ehlers-Danlos syndrome, unspecified

Q79.60Billable

Differential Codes

Alternative codes to consider when ruling out similar conditions

Hypermobility syndromeM35.7

Use for hypermobility without systemic manifestations of EDS.

Hypermobile Ehlers-Danlos syndromeQ79.62

Use for hypermobile EDS confirmed by Beighton score and systemic manifestations.

Classical Ehlers-Danlos syndromeQ79.61

Use for classical EDS confirmed by genetic testing.

Documentation & Coding Risks

Avoid these common issues when documenting Ehlers-Danlos Syndrome.

Failure to document genetic testing results

Impact

Clinical: May lead to inappropriate treatment plans., Regulatory: Non-compliance with coding standards., Financial: Potential for denied claims.

Mitigation

Ensure genetic test results are included in patient records., Verify documentation before coding.

Using unspecified EDS code when specific type is documented

Impact

Reimbursement: May lead to lower reimbursement rates., Compliance: Potential non-compliance with coding guidelines., Data Quality: Decreased accuracy in health records.

Mitigation

Ensure specific EDS type is coded when documentation supports it.

Use of unspecified codes

Impact

High risk of audit if unspecified codes are used without justification.

Mitigation

Ensure specific EDS type is documented and coded.

Frequently Asked Questions

Primary Code

Q79.60

Ehlers-Danlos syndrome, unspecified

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ICD-10 codes6

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