Documentation & Coding Risks
Avoid these common issues when documenting Hyperglycinemia.
Frequently Asked Questions
The ICD-10 code for nonketotic hyperglycinemia is E72.51, used when confirmed by clinical and genetic testing.
Diagnosis involves CSF glycine >200 μmol/L, CSF/plasma ratio >0.08, and genetic testing for GLDC or AMT mutations.
Related condition guides
Documentation requirements, coding pitfalls and FAQs for conditions coded with E72.51.