What is the ICD-10 code for hereditary hypogammaglobulinemia?

The ICD-10 code for hereditary hypogammaglobulinemia is D80.0, used when genetic testing confirms a hereditary form.

How is nonfamilial hypogammaglobulinemia coded?

Nonfamilial hypogammaglobulinemia is coded as D80.1, applicable when IgG levels are low without a family history.

ICD-10 Coding for Hypogammaglobulinemia(D80.0, D80.1, D80.7)

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Comprehensive guide on ICD-10 coding for hypogammaglobulinemia, including hereditary, nonfamilial, and transient forms. Learn about documentation requirements and coding pitfalls.

Also known as:

Immunoglobulin deficiencyLow immunoglobulin levelslow gamma globulin levels

Related ICD-10 Code Ranges

Complete code families applicable to Hypogammaglobulinemia

D50-D89Primary Range

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

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Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

Code	Description	When to Use	Key Documentation
D80.0	Hereditary hypogammaglobulinemia	Use when genetic testing confirms hereditary hypogammaglobulinemia.	Family history of immunodeficiency Genetic testing confirming specific mutations IgG levels < 200 mg/dL + 1 more
D80.1	Nonfamilial hypogammaglobulinemia	Use for acquired hypogammaglobulinemia without a family history.	IgG levels < 400 mg/dL Recurrent infections Normal B-cell count
D80.7	Transient hypogammaglobulinemia of infancy	Use for infants with temporary IgG deficiency resolving by age 3.	IgG levels < 300 mg/dL in infants Normalization of IgG by age 3

Primary ICD-10-CM Codes

Hereditary hypogammaglobulinemia

D80.0Billable

Differential Codes

Alternative codes to consider when ruling out similar conditions

Nonfamilial hypogammaglobulinemiaD80.1

Hereditary hypogammaglobulinemiaD80.0

Documentation & Coding Risks

Avoid these common issues when documenting Hypogammaglobulinemia.

Failure to document genetic testing for hereditary cases.

Impact

Clinical: May lead to misdiagnosis and inappropriate treatment., Regulatory: Non-compliance with coding standards., Financial: Potential for claim denials.

Mitigation

Ensure genetic testing is ordered and results are documented., Educate staff on documentation requirements.

Using D80.9 (Unspecified) when specific IgG levels are documented.

Impact

Reimbursement: May lead to claim denials or reduced reimbursement., Compliance: Non-compliance with coding guidelines., Data Quality: Decreases accuracy of patient records.

Mitigation

Query provider for specific type of hypogammaglobulinemia.

Documentation of IgG levels

Impact

Inadequate documentation of IgG levels can lead to audit issues.

Mitigation

Implement regular audits of patient records to ensure compliance.

Frequently Asked Questions

Documentation requirements, coding pitfalls and FAQs for conditions coded with D80.0.

Primary Code

D80.0

Hereditary hypogammaglobulinemia

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ICD-10 codes7

Coding risks3

FAQs2

ICD-10 Coding for Hypogammaglobulinemia(D80.0, D80.1, D80.7)

Documentation & Coding Risks

Frequently Asked Questions

What is the ICD-10 code for hereditary hypogammaglobulinemia?

How is nonfamilial hypogammaglobulinemia coded?

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