What is the ICD-10 code for Long QT Syndrome?

The ICD-10 code for Long QT Syndrome is I45.81. For congenital forms, use Q87.89 as an additional code.

How is Long QT Syndrome documented?

Documentation should include QTc measurements, genetic test results, and specify whether the condition is congenital or acquired.

ICD-10 Coding for Long QT Syndrome(I45.81, I45.8, I47.2)

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Learn about ICD-10 coding for Long QT Syndrome, including documentation requirements and common coding pitfalls.

Also known as:

Long QT IntervalLQTSRomano-Ward Syndrome

Related ICD-10 Code Ranges

Complete code families applicable to Long QT Syndrome

I00-I99Primary Range

Diseases of the circulatory system

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Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

Code	Description	When to Use	Key Documentation
I45.81	Long QT syndrome	Use for confirmed cases of Long QT Syndrome not specified as congenital.	QTc ≥480 ms in females ≥470 ms in males Genetic testing confirming pathogenic variant
Q87.89	Other specified congenital malformation syndromes	Use as an additional code for congenital forms of Long QT Syndrome.	Genetic confirmation of congenital syndrome Family history of sudden cardiac death

Primary ICD-10-CM Codes

Long QT syndrome

I45.81Billable

Differential Codes

Alternative codes to consider when ruling out similar conditions

Ventricular tachycardiaI47.2

Use when VT is the primary focus of treatment.

Ventricular fibrillationI49.0

Use when VF is documented and treated.

Documentation & Coding Risks

Avoid these common issues when documenting Long QT Syndrome.

Omitting QTc measurement in documentation

Impact

Clinical: Inadequate assessment of arrhythmia risk., Regulatory: Non-compliance with documentation standards., Financial: Potential denial of claims due to incomplete documentation.

Mitigation

Ensure QTc values are recorded in every patient encounter., Use standardized templates for documentation.

Coding syncope (R55) when arrhythmia is present

Impact

Reimbursement: Incorrect DRG assignment affecting reimbursement., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate clinical data representation.

Mitigation

Code I47.2 or I49.0 with I45.81 instead of R55.

Coding accuracy for Long QT Syndrome

Impact

Potential for miscoding congenital vs. acquired forms.

Mitigation

Implement regular training on coding guidelines and updates.

Frequently Asked Questions

Documentation requirements, coding pitfalls and FAQs for conditions coded with I45.81.

Primary Code

I45.81

Long QT syndrome

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ICD-10 codes7

Coding risks3

FAQs2

ICD-10 Coding for Long QT Syndrome(I45.81, I45.8, I47.2)

Documentation & Coding Risks

Frequently Asked Questions

What is the ICD-10 code for Long QT Syndrome?

How is Long QT Syndrome documented?

Related condition guides