Documentation & Coding Risks
Avoid these common issues when documenting Lung Fibroelastosis.
Frequently Asked Questions
The ICD-10 code for lung fibroelastosis, specifically pleuroparenchymal fibroelastosis (PPFE), is J84.178. Use J84.170 if the condition shows a progressive fibrotic phenotype.
Pleuroparenchymal fibroelastosis is diagnosed through HRCT showing upper lobe pleural thickening and biopsy confirming intra-alveolar fibrosis with septal elastosis.
Related condition guides
Documentation requirements, coding pitfalls and FAQs for conditions coded with J84.178.