What is the ICD-10 code for systemic mastocytosis?

The ICD-10 code for systemic mastocytosis is D47.02, used when systemic involvement is confirmed with bone marrow biopsy and elevated tryptase levels.

How is aggressive systemic mastocytosis coded?

Aggressive systemic mastocytosis is coded as C96.21, used when there is documented organ damage and C-findings.

ICD-10 Coding for Mastocytosis(D47.02, C96.2, C96.21)

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Comprehensive guide on ICD-10 coding for mastocytosis, including systemic and aggressive forms. Learn about documentation requirements and common pitfalls.

Also known as:

Mast cell diseaseSystemic mastocytosisCutaneous mastocytosis

Related ICD-10 Code Ranges

Complete code families applicable to Mastocytosis

C00-D49Primary Range

Neoplasms

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Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

Code	Description	When to Use	Key Documentation
D47.02	Systemic mastocytosis	Use when systemic involvement is confirmed with bone marrow biopsy and elevated tryptase levels.	Bone marrow biopsy showing ≥15 mast cell aggregates KIT D816V mutation Serum tryptase >20 ng/mL
C96.21	Aggressive systemic mastocytosis	Use when aggressive systemic involvement with organ damage is documented.	Organ damage such as cytopenias or hepatomegaly C-findings like ascites or hypoalbuminemia
D47.01	Cutaneous mastocytosis	Use when mastocytosis is limited to the skin without systemic involvement.	Positive Darier’s sign Skin biopsy with spindle-shaped mast cells
Q82.2	Congenital cutaneous mastocytosis	Use when mastocytosis is present from birth.	Documentation of congenital origin Presence since birth

Primary ICD-10-CM Codes

Systemic mastocytosis

D47.02Billable

Differential Codes

Alternative codes to consider when ruling out similar conditions

Other specified disorders involving the immune mechanism, not elsewhere classifiedD89.8

Systemic mastocytosisD47.02

Congenital cutaneous mastocytosisQ82.2

Cutaneous mastocytosisD47.01

Documentation & Coding Risks

Avoid these common issues when documenting Mastocytosis.

Inadequate documentation of systemic involvement

Impact

Clinical: May lead to misdiagnosis or inappropriate treatment., Regulatory: Non-compliance with coding standards., Financial: Potential loss of reimbursement.

Mitigation

Ensure detailed biopsy and laboratory findings are documented., Use specific terminology for systemic involvement.

Confusing systemic mastocytosis with mast cell activation syndrome

Impact

Reimbursement: Incorrect coding may lead to improper DRG assignment., Compliance: May result in non-compliance with coding standards., Data Quality: Affects accuracy of patient records and data analysis.

Mitigation

Ensure documentation meets systemic mastocytosis criteria before coding.

Documenting 'urticaria pigmentosa' without specifying congenital vs. acquired

Impact

Reimbursement: Incorrect code may affect reimbursement rates., Compliance: Non-compliance with ICD-10 coding guidelines., Data Quality: Leads to inaccurate patient data.

Mitigation

Confirm and document the onset of the condition.

Documentation of systemic involvement

Impact

Lack of detailed biopsy and laboratory findings.

Mitigation

Ensure comprehensive documentation of all diagnostic criteria.

Frequently Asked Questions

Documentation requirements, coding pitfalls and FAQs for conditions coded with D47.02.

Primary Code

D47.02

Systemic mastocytosis

Quick Navigation

ICD-10 codes11

Coding risks4

FAQs2

ICD-10 Coding for Mastocytosis(D47.02, C96.2, C96.21)

Documentation & Coding Risks

Frequently Asked Questions

What is the ICD-10 code for systemic mastocytosis?

How is aggressive systemic mastocytosis coded?

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