What is the ICD-10 code for sickle cell disease with crisis?

The ICD-10 code for sickle cell disease with crisis is D57.01 for HbSS with crisis and D57.219 for HbSC with crisis.

How do you document sickle cell crisis?

Document the genotype, crisis type, triggers, and any complications to ensure accurate coding and treatment planning.

ICD-10 Coding for Sickle Cell Disease with Crisis(D57.01, D57.0, D57.219)

Save

Learn about ICD-10 coding for sickle cell disease with crisis, including documentation requirements and common pitfalls.

Also known as:

Sickle Cell CrisisVaso-occlusive Crisis

Related ICD-10 Code Ranges

Complete code families applicable to Sickle Cell Disease with Crisis

D50-D89Primary Range

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

→

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

Code	Description	When to Use	Key Documentation
D57.01	HbSS with crisis	Use when a patient with HbSS genotype presents with an acute pain crisis.	Hgb electrophoresis showing HbSS Reticulocyte count >10% Pain crisis documentation
D57.219	HbSC with crisis	Use when a patient with HbSC genotype presents with an acute pain crisis.	Hb electrophoresis showing HbSC Documented pain crisis

Primary ICD-10-CM Codes

Hb-SS disease with acute chest syndrome

D57.01Billable

Differential Codes

Alternative codes to consider when ruling out similar conditions

HbSC with crisisD57.219

Use when Hb electrophoresis confirms HbSC genotype.

HbSS with crisisD57.01

Use when Hb electrophoresis confirms HbSS genotype.

Documentation & Coding Risks

Avoid these common issues when documenting Sickle Cell Disease with Crisis.

Failing to document crisis triggers

Impact

Clinical: Inadequate treatment planning., Regulatory: Non-compliance with documentation standards., Financial: Potential for denied claims.

Mitigation

Always ask about recent triggers during patient history.

Using unspecified codes for sickle cell crisis

Impact

Reimbursement: May lead to lower reimbursement rates., Compliance: Non-compliance with coding guidelines., Data Quality: Decreases accuracy of patient records.

Mitigation

Always specify the genotype and crisis type in documentation.

Genotype Documentation

Impact

Failure to document genotype can lead to audit issues.

Mitigation

Ensure genotype is documented in every case of sickle cell crisis.

Frequently Asked Questions

Documentation requirements, coding pitfalls and FAQs for conditions coded with D57.01.

Primary Code

D57.01

Hb-SS disease with acute chest syndrome

Quick Navigation

ICD-10 codes6

Coding risks3

FAQs2

ICD-10 Coding for Sickle Cell Disease with Crisis(D57.01, D57.0, D57.219)

Documentation & Coding Risks

Frequently Asked Questions

What is the ICD-10 code for sickle cell disease with crisis?

How do you document sickle cell crisis?

Related condition guides