What is the ICD-10 code for hereditary hemorrhagic telangiectasia?

The ICD-10 code for hereditary hemorrhagic telangiectasia is I78.0, used when clinical criteria or genetic testing confirms the diagnosis.

How do you code non-hereditary telangiectasia?

Non-hereditary telangiectasia is coded as I78.1, provided there is no systemic involvement or hereditary features.

What documentation is needed for HHT coding?

For HHT coding, document epistaxis frequency, family history, and presence of visceral AVMs to meet Curaçao criteria.

ICD-10 Coding for Telangiectasia(I78.0, I78.1, K31.89)

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Comprehensive guide on ICD-10 coding for telangiectasia, including hereditary and non-hereditary forms, with documentation requirements and coding tips.

Also known as:

Spider veinsAngioma serpiginosum

Related ICD-10 Code Ranges

Complete code families applicable to Telangiectasia

I00-I99Primary Range

Diseases of the circulatory system

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Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

Code	Description	When to Use	Key Documentation
I78.0	Hereditary hemorrhagic telangiectasia	Use when hereditary hemorrhagic telangiectasia is confirmed by clinical criteria or genetic testing.	Epistaxis Visceral AVMs Family history
I78.1	Non-neoplastic nevus	Use for localized telangiectasia without hereditary or systemic features.	Exclusion of hereditary criteria Site-specific documentation
K55.21	Angiodysplasia of colon without hemorrhage	Use when colonic telangiectasia is confirmed without active bleeding.	Endoscopic confirmation of vascular lesions

Primary ICD-10-CM Codes

Hereditary hemorrhagic telangiectasia

I78.0Billable

Differential Codes

Alternative codes to consider when ruling out similar conditions

Non-neoplastic nevusI78.1

Rosacea, unspecifiedL71.9

Use for rosacea-associated telangiectasia with erythema.

Documentation & Coding Risks

Avoid these common issues when documenting Telangiectasia.

Incomplete documentation of telangiectasia

Impact

Clinical: May lead to misdiagnosis or inappropriate treatment, Regulatory: Non-compliance with documentation standards, Financial: Potential claim denials or reduced reimbursement

Mitigation

Use structured templates for documentation, Ensure all clinical criteria are recorded

Using I78.1 alone for rectal telangiectasia

Impact

Reimbursement: Incorrect sequencing may lead to denied claims, Compliance: Non-compliance with coding guidelines, Data Quality: Inaccurate clinical data representation

Mitigation

Sequence K62.8 (rectum) → I78.1

Using retired code Q3638 for intestinal telangiectasia

Impact

Reimbursement: Claims may be rejected due to outdated coding, Compliance: Violation of current coding standards, Data Quality: Outdated data affecting clinical records

Mitigation

Use K55.21/K55.22 + I78.1

Telangiectasia coding

Impact

Incorrect sequencing or use of outdated codes

Mitigation

Regular training on current coding guidelines and updates

Frequently Asked Questions

Documentation requirements, coding pitfalls and FAQs for conditions coded with I78.0.

Primary Code

I78.0

Hereditary hemorrhagic telangiectasia

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ICD-10 codes6

Coding risks4

FAQs3

ICD-10 Coding for Telangiectasia(I78.0, I78.1, K31.89)

Documentation & Coding Risks

Frequently Asked Questions

What is the ICD-10 code for hereditary hemorrhagic telangiectasia?

How do you code non-hereditary telangiectasia?

What documentation is needed for HHT coding?

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