E83.821BillableSave
E83.821 - ENPP1 deficiency causing generalized arterial calcification of infancy
ICD-10-CM Chapter 4: Endocrine, nutritional and metabolic diseases · E70-E88 Metabolic disorders (E70-E88) · Subcategory of E83.82 · FY2027
Includes, Excludes and Coding Notes
Code AlsoFrom E83.821
Report an additional code when both conditions apply.
- , if applicable, associated conditions such as:
- heart failure (I50.-)
- other secondary hypertension (I15.8)
Excludes 1 — Not Coded HereFrom E83
Mutually exclusive: these conditions are never reported together with this code.
- dietary mineral deficiency (E58-E61)
- parathyroid disorders (E20-E21)
- vitamin D deficiency (E55.-)
Excludes 1 — Not Coded HereFrom E70-E88 Metabolic disorders (E70-E88)
Mutually exclusive: these conditions are never reported together with this code.
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
Excludes 2 — Not Included HereFrom E70-E88 Metabolic disorders (E70-E88)
Not part of this code; report both codes when the patient has both conditions.
- Ehlers-Danlos syndromes (Q79.6-)
Excludes 1 — Not Coded HereFrom Chapter E00-E89
Mutually exclusive: these conditions are never reported together with this code.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
NotesFrom Chapter E00-E89
Instructional notes from the ICD-10-CM tabular list.
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Related condition guides
Documentation requirements, coding pitfalls and FAQs for conditions coded with E83.821.
Chapter Information
Other codes in E83.82
Codes at the same level as E83.821
- Generalized arterial calcification of infancy with unspecified genetic causalityE83.820
- ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2E83.822
- ABCC6 deficiency causing generalized arterial calcification of infancyE83.823
- ABCC6 deficiency causing pseudoxanthoma elasticumE83.824
- CD73 deficiency causing arterial calcificationE83.825