I01Non-billableSave
I01 - Rheumatic fever with heart involvement
ICD-10-CM Chapter 9: Diseases of the circulatory system · I00-I02 Acute rheumatic fever (I00-I02) · Top-level category · FY2027
Coding Guidance
I01 is a non-billable heading. Report one of the 5 more specific codes below.
Includes, Excludes and Coding Notes
Excludes 1 — Not Coded HereFrom I01
Mutually exclusive: these conditions are never reported together with this code.
- chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.
Excludes 2 — Not Included HereFrom Chapter I00-I99
Not part of this code; report both codes when the patient has both conditions.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
More Specific Codes (5)
Related condition guides
Documentation requirements, coding pitfalls and FAQs for conditions coded with I01.
Chapter Information
Related ICD-10 Codes
More specific codes for I01
Other categories in this chapter
Codes at the same level as I01
- Rheumatic fever without heart involvementI00
- Rheumatic choreaI02
- Rheumatic mitral valve diseasesI05
- Rheumatic aortic valve diseasesI06
- Rheumatic tricuspid valve diseasesI07
- Multiple valve diseasesI08
- Other rheumatic heart diseasesI09
- Essential (primary) hypertensionI10
- Hypertensive heart diseaseI11
- Hypertensive chronic kidney diseaseI12
- Hypertensive heart and chronic kidney diseaseI13
- Secondary hypertensionI15
- Hypertensive crisisI16
- Other hypertensionI1A
- Angina pectorisI20
- Acute myocardial infarctionI21
- Subsequent ST elevation (STEMI) and non-ST elevation (NSTEMI) myocardial infarctionI22
- Certain current complications following ST elevation (STEMI) and non-ST elevation (NSTEMI) myocardial infarction (within the 28 day period)I23
- Other acute ischemic heart diseasesI24
- Chronic ischemic heart diseaseI25
- Pulmonary embolismI26
- Other pulmonary heart diseasesI27
- Other diseases of pulmonary vesselsI28
- Acute pericarditisI30
- Other diseases of pericardiumI31
- Pericarditis in diseases classified elsewhereI32
- Acute and subacute endocarditisI33
- Nonrheumatic mitral valve disordersI34
- Nonrheumatic aortic valve disordersI35
- Nonrheumatic tricuspid valve disordersI36
- Nonrheumatic pulmonary valve disordersI37
- Endocarditis, valve unspecifiedI38
- Endocarditis and heart valve disorders in diseases classified elsewhereI39
- Acute myocarditisI40
- Myocarditis in diseases classified elsewhereI41
- CardiomyopathyI42
- Cardiomyopathy in diseases classified elsewhereI43
- Atrioventricular and left bundle-branch blockI44
- Other conduction disordersI45
- Cardiac arrestI46
39 more in this chapter.