M04.3BillableSave New in FY2027

M04.3 - VEXAS syndrome

ICD-10-CM Chapter 13: Diseases of the musculoskeletal system and connective tissue · M04 Autoinflammatory syndromes (M04) · Subcategory of M04 · FY2027

Applicable To

Inclusion terms listed under M04.3 in the ICD-10-CM tabular list.

  • Vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic syndrome

Includes, Excludes and Coding Notes

Code AlsoFrom M04.3

Report an additional code when both conditions apply.

  • any associated conditions
Excludes 2 — Not Included HereFrom M04

Not part of this code; report both codes when the patient has both conditions.

  • Crohn's disease (K50.-)
Excludes 2 — Not Included HereFrom Chapter M00-M99

Not part of this code; report both codes when the patient has both conditions.

  • arthropathic psoriasis (L40.5-)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • compartment syndrome (traumatic) (T79.A-)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
NotesFrom Chapter M00-M99

Instructional notes from the ICD-10-CM tabular list.

  • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition