Q56Non-billableSave
Q56 - Indeterminate sex and pseudohermaphroditism
ICD-10-CM Chapter 17: Congenital malformations, deformations and chromosomal abnormalities · Q50-Q56 Congenital malformations of genital organs (Q50-Q56) · Top-level category · FY2027
Coding Guidance
Q56 is a non-billable heading. Report one of the 5 more specific codes below.
Includes, Excludes and Coding Notes
Excludes 1 — Not Coded HereFrom Q56
Mutually exclusive: these conditions are never reported together with this code.
- 46,XX true hermaphrodite (Q99.1)
- androgen insensitivity syndrome (E34.5-)
- chimera 46,XX/46,XY true hermaphrodite (Q99.0)
- female pseudohermaphroditism with adrenocortical disorder (E25.-)
- pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
- pure gonadal dysgenesis (Q99.1)
Excludes 1 — Not Coded HereFrom Q50-Q56 Congenital malformations of genital organs (Q50-Q56)
Mutually exclusive: these conditions are never reported together with this code.
- androgen insensitivity syndrome (E34.5-)
- syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)
Excludes 2 — Not Included HereFrom Chapter Q00-Q99
Not part of this code; report both codes when the patient has both conditions.
- inborn errors of metabolism (E70-E88)
NotesFrom Chapter Q00-Q99
Instructional notes from the ICD-10-CM tabular list.
- Codes from this chapter are not for use on maternal records
More Specific Codes (5)
Chapter Information
Chapter 17: Congenital malformations, deformations and chromosomal abnormalities
Range: Q00-Q99
View full chapterRelated ICD-10 Codes
More specific codes for Q56
Other categories in this chapter
Codes at the same level as Q56
- Anencephaly and similar malformationsQ00
- EncephaloceleQ01
- MicrocephalyQ02
- Congenital hydrocephalusQ03
- Other congenital malformations of brainQ04
- Spina bifidaQ05
- Other congenital malformations of spinal cordQ06
- Other congenital malformations of nervous systemQ07
- Congenital malformations of eyelid, lacrimal apparatus and orbitQ10
- Anophthalmos, microphthalmos and macrophthalmosQ11
- Congenital lens malformationsQ12
- Congenital malformations of anterior segment of eyeQ13
- Congenital malformations of posterior segment of eyeQ14
- Other congenital malformations of eyeQ15
- Congenital malformations of ear causing impairment of hearingQ16
- Other congenital malformations of earQ17
- Other congenital malformations of face and neckQ18
- Congenital malformations of cardiac chambers and connectionsQ20
- Congenital malformations of cardiac septaQ21
- Congenital malformations of pulmonary and tricuspid valvesQ22
- Congenital malformations of aortic and mitral valvesQ23
- Other congenital malformations of heartQ24
- Congenital malformations of great arteriesQ25
- Congenital malformations of great veinsQ26
- Other congenital malformations of peripheral vascular systemQ27
- Other congenital malformations of circulatory systemQ28
- Congenital malformations of noseQ30
- Congenital malformations of larynxQ31
- Congenital malformations of trachea and bronchusQ32
- Congenital malformations of lungQ33
- Other congenital malformations of respiratory systemQ34
- Cleft palateQ35
- Cleft lipQ36
- Cleft palate with cleft lipQ37
- Other congenital malformations of tongue, mouth and pharynxQ38
- Congenital malformations of esophagusQ39
- Other congenital malformations of upper alimentary tractQ40
- Congenital absence, atresia and stenosis of small intestineQ41
- Congenital absence, atresia and stenosis of large intestineQ42
- Other congenital malformations of intestineQ43
48 more in this chapter.