Q89.81BillableSave
Q89.81 - Kabuki syndrome
ICD-10-CM Chapter 17: Congenital malformations, deformations and chromosomal abnormalities · Q80-Q89 Other congenital malformations (Q80-Q89) · Subcategory of Q89.8 · FY2027
Applicable To
Inclusion terms listed under Q89.81 in the ICD-10-CM tabular list.
- Kabuki syndrome, type 1, due to KMT2D mutation
- Kabuki syndrome, type 2, due to KDM6A mutation
- Niikawa-Kuroki syndrome
Includes, Excludes and Coding Notes
Use Additional CodeFrom Q89.8
Add a secondary code to identify the associated condition or cause when it is documented.
- code(s) to identify all associated manifestations
Excludes 2 — Not Included HereFrom Chapter Q00-Q99
Not part of this code; report both codes when the patient has both conditions.
- inborn errors of metabolism (E70-E88)
NotesFrom Chapter Q00-Q99
Instructional notes from the ICD-10-CM tabular list.
- Codes from this chapter are not for use on maternal records
Related condition guides
Documentation requirements, coding pitfalls and FAQs for conditions coded with Q89.81.
Chapter Information
Chapter 17: Congenital malformations, deformations and chromosomal abnormalities
Range: Q00-Q99
View full chapterOther codes in Q89.8
Codes at the same level as Q89.81