Q87.ABillableSave New in FY2027
Q87.A - Loeys-Dietz syndrome
ICD-10-CM Chapter 17: Congenital malformations, deformations and chromosomal abnormalities · Q80-Q89 Other congenital malformations (Q80-Q89) · Subcategory of Q87 · FY2027
Includes, Excludes and Coding Notes
Excludes 1 — Not Coded HereFrom Q87.A
Mutually exclusive: these conditions are never reported together with this code.
- arterial tortuosity syndrome (Q87.82)
- Ehlers-Danlos syndrome (Q79.6)
- Marfan syndrome (Q87.40-Q87.43)
- other systemic involvement of connective tissue (M35)
Use Additional CodeFrom Q87
Add a secondary code to identify the associated condition or cause when it is documented.
- code(s) to identify all associated manifestations
Excludes 2 — Not Included HereFrom Chapter Q00-Q99
Not part of this code; report both codes when the patient has both conditions.
- inborn errors of metabolism (E70-E88)
NotesFrom Chapter Q00-Q99
Instructional notes from the ICD-10-CM tabular list.
- Codes from this chapter are not for use on maternal records
Related condition guides
Documentation requirements, coding pitfalls and FAQs for conditions coded with Q87.A.
Chapter Information
Chapter 17: Congenital malformations, deformations and chromosomal abnormalities
Range: Q00-Q99
View full chapterOther codes in Q87
Codes at the same level as Q87.A
- Congenital malformation syndromes predominantly affecting facial appearanceQ87.0
- Congenital malformation syndromes predominantly associated with short statureQ87.1
- Congenital malformation syndromes predominantly involving limbsQ87.2
- Congenital malformation syndromes involving early overgrowthQ87.3
- Marfan syndromeQ87.4
- Other congenital malformation syndromes with other skeletal changesQ87.5
- Other specified congenital malformation syndromes, not elsewhere classifiedQ87.8